Table 4 The World Health Organization classification (2010)

Appendiceal carcinomas.

• Adenocarcinoma 8140/3

• Mucinous adenocarcinoma 8480/3

• Low-grade mucinous neoplasia 8480/1

• Signet-ring cell formation carcinoma 8490/3

• Undifferentiated carcinoma 8020/3

Neuroendocrine appendix neoplasias.

• Neuroendocrine tumors (NET).

• NET G1 (carcinoid) 8240/3

• NET G2 8249/3

• Neuroendocrine carcinomas (NEC) 8246/3

• NEC large cells type 8013/3

• NEC smal cells type 8041/3

• Mixed tumor:

• Mixed Adenoneuroendocrine carcinomas 8244/3

• Serotonin-producing endocrine carcinoma 8241/3

• Globet cell carcinoid 8243/3

• Tubular carcinoid 8245/1

• Peptide-producing/ Glucagon-producing large cell tumor PP/PYY 8152/1